Clinical presentation and therapeutic approach of a pulmonary cystic adenomatoid malformation type III

Authors

Keywords:

lung malformation, congenital, type III, neonates, lobectomy

Abstract

Pulmonary cystic adenomatoid adenomatoid malformation (PCAM) type III is a rare congenital anomaly characterized by a solid lung mass composed of immature bronchiolar structures. It usually presents in neonates with severe respiratory distress, as occurred in the case under discussion. The diagnosis was confirmed by computed tomography of the thorax, showing a hyperdense mass without cavity formation. Surgical treatment was performed by pulmonary lobectomy, with favorable postoperative evolution. The histopathological study confirmed the diagnosis of type III PCMA. This case highlights the importance of early differential diagnosis of congenital pulmonary masses in newborns and underlines the need for a multidisciplinary approach for successful management. Long-term clinical and radiological follow-up is recommended to rule out respiratory complications or recurrences.

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Published

2025-11-12

How to Cite

1.
Guevara García YT, Guijarro Reinoso GP, Laica Sailema SA. Clinical presentation and therapeutic approach of a pulmonary cystic adenomatoid malformation type III. CCM [Internet]. 2025 Nov. 12 [cited 2026 Mar. 1];29:e5411. Available from: https://revcocmed.sld.cu/index.php/cocmed/article/view/5411