Clinical presentation and therapeutic approach of a pulmonary cystic adenomatoid malformation type III
Keywords:
lung malformation, congenital, type III, neonates, lobectomyAbstract
Pulmonary cystic adenomatoid adenomatoid malformation (PCAM) type III is a rare congenital anomaly characterized by a solid lung mass composed of immature bronchiolar structures. It usually presents in neonates with severe respiratory distress, as occurred in the case under discussion. The diagnosis was confirmed by computed tomography of the thorax, showing a hyperdense mass without cavity formation. Surgical treatment was performed by pulmonary lobectomy, with favorable postoperative evolution. The histopathological study confirmed the diagnosis of type III PCMA. This case highlights the importance of early differential diagnosis of congenital pulmonary masses in newborns and underlines the need for a multidisciplinary approach for successful management. Long-term clinical and radiological follow-up is recommended to rule out respiratory complications or recurrences.
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